Cookies on this website
We use cookies to ensure that we give you the best experience on our website. If you click 'Continue' we'll assume that you are happy to receive all cookies and you won't see this message again. Click 'Find out more' for information on how to change your cookie settings.

Scleroderma is a rare disease with limited data on its occurrence. Published prevalence rates vary widely with contemporary studies based on hospital ascertained cases, reporting rates of 30-120/million population. The annual incidence of new cases is much lower with rates of 2-20/million/year. Rates are substantially higher in females with a peak onset in the fifth and sixth decade. The disease is associated with a substantially reduced survival with approximately 50% surviving 10 years. Again, there is wide variation among studies probably reflecting patient selection factors. Apart from an increased risk of death from scleroderma related causes, there is also an increased cancer mortality particularly of the lung.

Type

Journal article

Journal

The Journal of rheumatology. Supplement

Publication Date

05/1997

Volume

48

Pages

58 - 61

Addresses

ARC Epidemiology Research Unit, University of Manchester, UK.

Keywords

Humans, Scleroderma, Systemic, Incidence, Survival Rate, Risk Factors, Age Distribution, Sex Distribution, Adult, Middle Aged, United States, Europe, New Zealand, Female, Male